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GAA Stabilizer 21

 

CAS: N/A

 

Chemical Name: 1,4-Dideoxy-1,4-imino-L-arabinitol; (2S,3S,4S)-2-(Hydroxymethyl)pyrrolidine-3,4-diol

 

 
GLXC-26785For Lab R&D Uses Only
        Cat No: GLXC-26785

 

Purity:               >98% (HPLC)

Storage:             Refrigerator (4 °C)

 

 

Product Description:

Novel acid alpha-glucosidase (GAA) stabilizer, preventing rh-GAA from denaturation, showing a 5.1-fold increase in rh-GAA activity in Pompe fibroblasts

 

Reference:

https://www.sciencedirect.com/science/article/abs/pii/S0968089622005223

 

Analytical data click for PDF file

 

 

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